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Solid Pseudo-Papillary Neoplasm of Pancreas: An Unusual Presentation and Management

Sandeep Kumar Jha, Vivek Mangla, Shailendra Lalwani, Sidhartha Mehrotra, Nita Radhakrishnan, Shefali Agarwal, Anupam Sachdeva, Samiran Nundy, Naimish Mehta

Solid pseudo-papillary neoplasms are rare, indolent pancreatic tumours in young women. We report an acute, large ruptured solid pseudo-papillary neoplasms in a child. At index surgery only de-bulking with control of haemorrhage was done in view of extensive, multi-organ resection. Four cycles of chemotherapy allowed us to downstage the tumour and subsequently a distal pancreatectomy with splenectomy was able to achieve negative margins. Patient was asymptomatic and without recurrence at 12 months. This case is being reported for the rarity of the tumour in this age group as well as for the difference in treatment strategy adopted because of the unusual presentation.